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Pulmonary Alveolar Microlithiasis and Rheumatoid Arthritis with Pulmonary Tuberculosis

Received: 27 June 2018     Accepted: 23 July 2018     Published: 24 August 2018
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Abstract

Pulmonary alveolar microlithiasis (PAM) is a rare autosomal recessive disease, characterised by widespread intra-alveolar accumulation of microliths. A 30-year-old male patient, known case of rheumatioid arthritis on treatment, presented with occasional complaints of cough with expectoration, since 1 year. He was found to be sputum AFB positive for which AKT was started, and a chest xray was advised, which showed diffuse bilateral micronodular calcific opacities having sand-like appearance distributed throughout the lungs, with a evident black pleural sign, which made us suspect PAM. An HRCT chest showed, multiple dense micronodular opacities in bilateral lung parenchyma prominently in the middle and lower lung zones giving a classical sandstorm appearance with sparing of a thin peripheral subpleural rim of parenchyma, giving a black pleura sign. The patient was symptomatically treated and was counselled for lung transplant and presents for regular follow up.

Published in American Journal of Internal Medicine (Volume 6, Issue 5)
DOI 10.11648/j.ajim.20180605.12
Page(s) 94-98
Creative Commons

This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited.

Copyright

Copyright © The Author(s), 2018. Published by Science Publishing Group

Keywords

Alveolar Microlithiasis, Rheumatoid Arthritis, Sputum Positive Pulmonary Tuberculosis

References
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[6] Al-Sardar H, Al-Habbo DJ, Al-Hayali RM Pulmonary alveolar microlithiasis: report of two brothers with the same illness and review of literature. BMJ Case Rep. 2014 Mar 31; 2014. pii: bcr2013201300. doi: 10.1136/bcr-2013-201300. Review. PMID: 24686795.
[7] La casistica della Puglia. Rass Pat App Respir Microlitiasi alveolare polmonare: proposta di iter diagnostico ottimale 2004; 19: 323–328. Castellana G.
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Cite This Article
  • APA Style

    Arti Sharma, Abhay Uppe, Shahid Patel, Girija Nair. (2018). Pulmonary Alveolar Microlithiasis and Rheumatoid Arthritis with Pulmonary Tuberculosis. American Journal of Internal Medicine, 6(5), 94-98. https://doi.org/10.11648/j.ajim.20180605.12

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    ACS Style

    Arti Sharma; Abhay Uppe; Shahid Patel; Girija Nair. Pulmonary Alveolar Microlithiasis and Rheumatoid Arthritis with Pulmonary Tuberculosis. Am. J. Intern. Med. 2018, 6(5), 94-98. doi: 10.11648/j.ajim.20180605.12

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    AMA Style

    Arti Sharma, Abhay Uppe, Shahid Patel, Girija Nair. Pulmonary Alveolar Microlithiasis and Rheumatoid Arthritis with Pulmonary Tuberculosis. Am J Intern Med. 2018;6(5):94-98. doi: 10.11648/j.ajim.20180605.12

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  • @article{10.11648/j.ajim.20180605.12,
      author = {Arti Sharma and Abhay Uppe and Shahid Patel and Girija Nair},
      title = {Pulmonary Alveolar Microlithiasis and Rheumatoid Arthritis with Pulmonary Tuberculosis},
      journal = {American Journal of Internal Medicine},
      volume = {6},
      number = {5},
      pages = {94-98},
      doi = {10.11648/j.ajim.20180605.12},
      url = {https://doi.org/10.11648/j.ajim.20180605.12},
      eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ajim.20180605.12},
      abstract = {Pulmonary alveolar microlithiasis (PAM) is a rare autosomal recessive disease, characterised by widespread intra-alveolar accumulation of microliths. A 30-year-old male patient, known case of rheumatioid arthritis on treatment, presented with occasional complaints of cough with expectoration, since 1 year. He was found to be sputum AFB positive for which AKT was started, and a chest xray was advised, which showed diffuse bilateral micronodular calcific opacities having sand-like appearance distributed throughout the lungs, with a evident black pleural sign, which made us suspect PAM. An HRCT chest showed, multiple dense micronodular opacities in bilateral lung parenchyma prominently in the middle and lower lung zones giving a classical sandstorm appearance with sparing of a thin peripheral subpleural rim of parenchyma, giving a black pleura sign. The patient was symptomatically treated and was counselled for lung transplant and presents for regular follow up.},
     year = {2018}
    }
    

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    T1  - Pulmonary Alveolar Microlithiasis and Rheumatoid Arthritis with Pulmonary Tuberculosis
    AU  - Arti Sharma
    AU  - Abhay Uppe
    AU  - Shahid Patel
    AU  - Girija Nair
    Y1  - 2018/08/24
    PY  - 2018
    N1  - https://doi.org/10.11648/j.ajim.20180605.12
    DO  - 10.11648/j.ajim.20180605.12
    T2  - American Journal of Internal Medicine
    JF  - American Journal of Internal Medicine
    JO  - American Journal of Internal Medicine
    SP  - 94
    EP  - 98
    PB  - Science Publishing Group
    SN  - 2330-4324
    UR  - https://doi.org/10.11648/j.ajim.20180605.12
    AB  - Pulmonary alveolar microlithiasis (PAM) is a rare autosomal recessive disease, characterised by widespread intra-alveolar accumulation of microliths. A 30-year-old male patient, known case of rheumatioid arthritis on treatment, presented with occasional complaints of cough with expectoration, since 1 year. He was found to be sputum AFB positive for which AKT was started, and a chest xray was advised, which showed diffuse bilateral micronodular calcific opacities having sand-like appearance distributed throughout the lungs, with a evident black pleural sign, which made us suspect PAM. An HRCT chest showed, multiple dense micronodular opacities in bilateral lung parenchyma prominently in the middle and lower lung zones giving a classical sandstorm appearance with sparing of a thin peripheral subpleural rim of parenchyma, giving a black pleura sign. The patient was symptomatically treated and was counselled for lung transplant and presents for regular follow up.
    VL  - 6
    IS  - 5
    ER  - 

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Author Information
  • Department of Pulmonary Medicine, D. Y. Patil Medical College, Navi Mumbai, India

  • Department of Pulmonary Medicine, D. Y. Patil Medical College, Navi Mumbai, India

  • Department of Pulmonary Medicine, D. Y. Patil Medical College, Navi Mumbai, India

  • Department of Pulmonary Medicine, D. Y. Patil Medical College, Navi Mumbai, India

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